The high interventricular septal defect which is situated between the pulmonary valve and the crista supraventricularis, differs in a surgical opinion from the other types of this malformation, because it may be possibly complicated with aortic incompetence. In 4 of 11 cases who have been operated upon for the last 2 years, harsh systolic murmurs with a maximum intensity in the 2nd. intercostral soace left to the sternum were heard. Cardiac catheterization revealed that there was an increase in oxygen content in the pulmonary trumk in 3 cases and in the conus arteriosus beneath the pulmonary valve in 1 case. Accordingly, this type of interventricular septal defect is not always easily differentiated preoperatively.