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Two Cases in Glycogenosis Type Ⅳ.Ⅰ. Light Microscopic Observation.

The bulletin of the Yamaguchi Medical School Volume 21 Issue 1-4 Page 91-101
published_at 1974-12
A020021000107.pdf
[fulltext] 1.75 MB
Title
Two Cases in Glycogenosis Type Ⅳ.Ⅰ. Light Microscopic Observation.
Creators Ishihara Tokuhiro
Creators Uchino Fumiya
Creators Adachi Hironobu
Creators Takahashi Mutsuo
Creators Watanabe Seishiro
Creators Onishi Hiromi
Creators Ikee Yoshihiko
Creators Misawa Sachiyo
Source Identifiers
glycogenosis type Ⅳ, which is characterized by deposits of polysaccharide in the liver and liver cirrhosis resembling postencratic type, were described in two children. They were siblings, had a sister with an identical disease and had unrelated parents. Furthermore, in one case in which a partial autopsy was performed, two kind of the polysaccharide were noted in the cardiac muscle, skeletal muscle, smooth muscle and reticuloendothelial cells. The one was normal glycogen and the other was not identical with normal glycogen because of its diastase resistance. The genesis of the cirrhosis may have been a reaction to the stimulation by the polysaccharide as a foreign body.
Subjects
医学 ( Other)
Languages eng
Resource Type departmental bulletin paper
Publishers Yamaguchi University Graduate School of Medicine
Date Issued 1974-12
File Version Version of Record
Access Rights open access
Relations
[ISSN]0513-1812
[NCID]AA00594272
Schools 医学部