Anesthetic management of a patient with gorham-stout syndrome for ventriculo-peritoneal shunt operation

Gorham-Stout症候群の21歳女性に対し,脳室腹腔シャント術の全身麻酔を行った.頭痛と複視の発症を契機に特発性頭蓋内圧亢進症の診断を受け,当院脳神経外科で腰椎ドレナージ術の治療を受けた後に,脳室腹腔シャント術を全身麻酔下に施行した.気管挿管にはエアウェイスコープ^{TM}を用いて慎重に気道確保を行い,麻酔維持はプロポフォールとレミフェンタニルを用いて安全な麻酔を行うことができた.術後,集中治療室に予定入室し経過観察したあと,明らかな問題なく翌日に病棟へ退室した.

A 21-year-old female patient, who was previously diagnosed with Gorham-Stout syndrome, underwent ventriculo-peritoneal shunt operation under general anesthesia. She was diagnosed with idiopathic intracranial hypertension presented with headache and diplopia, and treated with spinal drainage and ventriculo-peritoneal shunt operation under general anesthesia. In order to preserve her airway cautiously, Airway Scope^{TM} was used for tracheal intubation, and the anesthesia was maintained safely with propofol and remifentanil. After the surgery, she was observed in the intensive care unit on schedule, and was transferred back to the general ward on the first postoperative day, with no serious complications.

Gorham-Stout症候群

骨融解　

特発性頭蓋内圧亢進症　

脳室腹腔シャント術　

全身麻酔