The bulletin of the Yamaguchi Medical School
Continued by：Medical Science & Innovation
EISSN：2758-5441
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The bulletin of the Yamaguchi Medical School Volume 38 Issue 1-2
published_at 1991-06
A case of Rimmed Vacuole Myopathy with Limb-girdle Atrophy and Boule Musculaire
A case of Rimmed Vacuole Myopathy with Limb-girdle Atrophy and Boule Musculaire
Takase Yoshitaka
Yamagata Miki
Yamamoto Kiyoshi
Fukusako Toshihiro
Morimatsu Mitsunori
Kawazawa Syuhei
About This Article
Descriptions
A case of 58-year-old man with rimmed vacoule myopathy was reported, who had limb-girdle distribution of muscle weakness and atrophy, and had a boule musculaire in the left quadriceps muscle. Muscle biopsy was done in the quadriceps muscle neighbouring boule musculaire, and the specimen showed rimmed vacuoles in 7.6% of the muscle fibers, which appeared mainly in the border between muscle fibers and degenerative fat. Almost all of the rimmed vacuoles were observed in type 1 fibers, and occupied with many membranous whorls and myelin debris.
Creator Keywords
Rimmed vacuole
Myopathy
Proximal artophy
Boule musculaire
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